Rhabdomyomatous mesenchymal hamartoma presenting as a skin tag in a newborn
نویسندگان
چکیده
RMH: rhabdomyomatous mesenchymal hamartoma INTRODUCTION Rhabdomyomatous mesenchymal hamartoma (RMH) is a rare congenital lesion in the dermal and subcutaneous tissues of newborns that was first described as a striated muscle hamartoma in 1986 and named in 1989. Since then, 65 cases have been reported in the literature, some in association with other congenital abnormalities. Most cases have been described in young patients on the head and neck, but cases have also been reported on the tongue, perianal region, vagina, and great toe. On histologic examination, RMH consists of striated muscle bundles, adipose tissue, blood vessels, collagen, and nerves. We report a case of a solitary RMH presenting as a skin tag on the midline chin of a newborn boy.
منابع مشابه
Rhabdomyomatous Mesenchymal Hamartoma Presenting as a Midline Mass on a Chin
A 17-month-old boy was evaluated for a midline mass on his chin. The mass was anchored to the mentalis muscle with a stalk-like structure. The pathological diagnosis of the mass was rhabdomyomatous mesenchymal hamartoma. This is the first report of rhabdomyomatous mesenchymal hamartoma presenting as a midline chin mass in Korean pediatric patients.
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Rhabdomyomatous mesenchymal hamartoma (RMH) is a benign, rare entity with approximately 70 cases reported since the 1980’s [1]. This was first described in 1986 as a striated muscle hamartoma [1]. It has also been reported as congenital midline hamartoma and hamartoma of cutaneous adnexa and mesenchyme [1]. RMH most often presents as a solitary lesion on the head or neck of an infant [2]. The l...
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Rhabdomyomatous mesenchymal hamartoma is a rare congenital lesion which consists of randomly arranged striated muscle fibers interspersed with mesenchymal elements. We describe the clinical and histopathological features of a rhabdomyomatous mesenchymal hamartoma in a one year-old patient presenting a bilobulated lesion in the mid-cervical line. No associated congenital malformations were obser...
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Rhabdomyomatous hamartoma is a rare disease that occurs predominantly in the skin. This paper describes a congenital lesion in a 17-year-old male, who came to our clinic presenting a circumscribed swelling involving the oral mucosa and vermillion border of the upper lip, purplish in color, and blanching under pressure. The patient reported that he had had lesion since his birth. A clinical diag...
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